Clinic of Heart and Vascular Medicine, Vilnius University, Lithuania.
Medicina (Kaunas). 2010;46(3):193-9.
Isolated noncompaction of the ventricular myocardium is defined as a rare cardiomyopathy caused by intrauterine arrest of compaction of the myocardial fibers and meshwork, an important process in myocardial development, in absence of any coexisting congenital heart lesions. A lot of controversies exist about diagnostic criteria, nomenclature, origin, pathogenesis, and prognosis of this disease. Here, we describe an adult patient with isolated left ventricular noncompaction who presented with worsening congestive heart failure and was successfully treated with heart transplantation.
孤立性心室心肌致密化不全定义为一种罕见的心肌病，由心肌纤维和网架的宫内致密化阻滞引起，这是心肌发育的一个重要过程，而不存在任何并存的先天性心脏病变。对于该病的诊断标准、命名、起源、发病机制和预后存在很多争议。在这里，我们描述了 1 例成人孤立性左心室心肌致密化不全患者，该患者因充血性心力衰竭恶化而就诊，并成功接受了心脏移植治疗。
