Department of Radiology, Georgetown University Hospital, 3800 Reservoir Rd., N.W.,Washington, DC,20007, USA.
Pediatr Radiol. 2010 Dec;40 Suppl 1:S123-6. doi: 10.1007/s00247-010-1732-5. Epub 2010 Jun 5.
Primitive neuroectodermal tumors (PNETs) include a heterogeneous group that originate from primitive neuroepithelial cells. PNETs are prone to cerebrospinal fluid seeding and central nervous system spread. Infratentorial PNET, or medulloblastoma, is a common brain tumor in children and metastatic spread to the abdomen via a ventriculoperitoneal (VP) shunt has been described. Supratentorial PNETs are much less common. We present a rare case of a predominantly supratentorial PNET metastasizing to the abdomen via a VP shunt and discuss the radiological findings. This case demonstrates the small but real risk of metastatic spread, which should be weighed when considering VP shunt placement.
原始神经外胚层肿瘤（PNETs）包括一组起源于原始神经上皮细胞的异质性肿瘤。PNETs 易发生脑脊液播散和中枢神经系统扩散。后颅窝 PNET，又称髓母细胞瘤，是儿童常见的脑肿瘤，已有通过脑室-腹腔（VP）分流器转移至腹部的描述。幕上 PNET 则较为少见。我们报告了一例罕见的主要发生于幕上的 PNET 通过 VP 分流器转移至腹部的病例，并讨论了其影像学表现。该病例提示了存在转移扩散的微小但确实存在的风险，在考虑 VP 分流器放置时应权衡这一风险。
