Rieu P N, de Vries J D, Gardeniers J W, Bakker-Niezen S H
Afd. Kinderchirurgie, Universitair Centrum voor Chirurgie bij Kinderen Nijmegen.
Tijdschr Kindergeneeskd. 1991 Apr;59(2):58-64.
Vesico-intestinal fissure or exstrophy of the cloaca is a rare but serious birth defect of the urogenital tract and distal part of the digestive tract. The most important hallmarks are: bladder exstrophy, fusion between bladder and the exstrophied iliocoecal region, short blind-ending colon and imperforate anus. In addition the lower part of the body shows defects of the abdominal wall, symphysis, upper urinary tract, the internal and external genitals, lumbosacral spine, spinal cord and the lower extremities. It is just after 1960 that corrective surgery started to become successful. Because of the complexity of the anomaly it seems that only management by a team of specialists in a centre for pediatric surgery guarantees optimal treatment. The quality of live of these children can still be improved by application of the newest surgical techniques and excellent cooperation between the different involved specialists. The defects, surgical treatment and results in eight patients with vesico-intestinal fissure, seen at the Universitair Centrum voor Chirurgie bij Kinderen Nijmegen (UCCKN) from 1974 till 1989 inclusive, are presented.
膀胱肠裂或泄殖腔外翻是一种罕见但严重的泌尿生殖道和消化道远端的出生缺陷。最重要的特征是：膀胱外翻、膀胱与外翻的回盲部区域融合、短的盲端结肠和肛门闭锁。此外，身体下部还表现出腹壁、耻骨联合、上尿路、内外生殖器、腰骶椎、脊髓和下肢的缺陷。直到1960年后矫正手术才开始取得成功。由于该畸形的复杂性，似乎只有在小儿外科中心由一组专家进行管理才能保证最佳治疗。通过应用最新的手术技术以及不同相关专家之间的出色合作，这些儿童的生活质量仍可得到改善。本文介绍了1974年至1989年（含）在奈梅亨大学儿童外科中心（UCCKN）诊治的8例膀胱肠裂患者的缺陷、手术治疗及结果。
