Singh Bhupendra P, Pathak Hemant R, Andankar Mukund G
Department of Urology, BYL Nair Charitable Hospital and Topiwala National Medical College, Mumbai Central, Mumbai - 400 008, India.
Indian J Urol. 2010 Jan-Mar;26(1):126-8. doi: 10.4103/0970-1591.60460.
A 5-year-old female presented with continuous dribbling of urine without any voiding stream since birth. Upon investigations, the bladder neck and both ureters were opening into the vaginalized urogenital sinus and the urethra was absent. Coarctation of the aorta was an associated anomaly. To our knowledge, this is the first report in literature of bilateral single-system ectopic ureters opening into vaginalized urogenital sinus. The report highlights the necessity for consideration of continent diversion in such cases because of the absence of the urethra in addition to an incontinent bladder neck and tiny dysfunctional bladder.
一名5岁女性自出生以来一直存在持续性滴尿,无排尿流。经检查,膀胱颈和双侧输尿管均开口于阴道化的泌尿生殖窦,且尿道缺如。主动脉缩窄是一种相关的异常情况。据我们所知,这是文献中首例双侧单系统异位输尿管开口于阴道化泌尿生殖窦的报道。该报告强调了在此类病例中考虑可控性尿流改道的必要性,因为除了失禁的膀胱颈和功能不良的小膀胱外,还存在尿道缺如的情况。