The University Hospital, College of Medicine, Al-Nahrain University, Kadhimiya, Baghdad, Iraq.
Cardiol J. 2010;17(2):172-8.
Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is a disorder that involves replacement of the right ventricular myocardium with fibro-fatty tissue. Ventricular tachycardia is a main presenting feature. There are no known reports of this disease from the Arab countries in the Middle East. This is the first report of 34 patients from Iraq.
Thirty four patients with ARVC/D diagnosed from January 2003 to May 2007 according to the International Task Force criteria were included in this study.
All patients presented with ventricular tachycardia of left bundle branch block morphology. The following findings were seen on the 12-lead electrocardiography during sinus rhythm: T wave inversion V1-V3 or beyond in 80%, epsilon wave in 28%, and parietal block in 48%. Right ventricular enlargement by echocardiography was seen in 69%. Twenty two per cent had a family history of sudden cardiac death. All patients were treated with implanted cardioverter-defibrillators.
ARVC/D is a disease seen in Iraq. It requires a high diagnostic suspicion with verification using the international task force criteria.
致心律失常性右室心肌病/发育不良（ARVC/D）是一种涉及右心室心肌被纤维脂肪组织取代的疾病。室性心动过速是其主要表现特征。目前尚无来自中东阿拉伯国家的关于这种疾病的报道。这是来自伊拉克的 34 例患者的首例报告。
根据国际工作组标准，本研究纳入了 2003 年 1 月至 2007 年 5 月期间被诊断为 ARVC/D 的 34 例患者。
所有患者均表现为左束支传导阻滞形态的室性心动过速。窦性心律时 12 导联心电图可见以下表现：80%的患者 V1-V3 或以上导联 T 波倒置，28%的患者出现 ε 波，48%的患者出现心前区阻滞。超声心动图显示右心室扩大 69%。22%的患者有家族性心源性猝死史。所有患者均接受了植入式心脏复律除颤器治疗。
ARVC/D 在伊拉克较为常见。需要高度怀疑该病，并使用国际工作组标准进行确诊。
