Khiari Hela Mrabet, Chehaider Hend Batti, Mrabet Amel
Neurological Department, Charles Nicolle Hospital, Tunis, Tunisia.
Tunis Med. 2010 Jul;88(7):516-8.
Idiopathic childhood occipital epilepsy of Gastaut is a rare but well defined syndrome within the group of idiopathic focal epilepsies in childhood. Clinical manifestations are characterized by simple partial seizures with mainly visual symptoms followed by secondary generalization.
Report of a case of Childhood Occipital Epilepsy.
We report a case of 10-year-old-girl, with no history. At the age of 9 years, the patient started experiencing repetitive events without fever. The first event consisted of several episodes of loss of consciousness with hypotonia and post ictal amnesia. The second type was three episodes of stereotyped, elaborated complex visual hallucinations, during 10 minutes. One month later, a third type of tonico-clonic generalized seizures appeared. Neurological examination and routine laboratory investigation were normal. Brain neuroimaging was normal. Interictal EEG showed bilateral discharges of slow generalized waves activated by hyperventilation. She has been treated by Sodium Valproate. All seizures stopped and she remained free of seizures.
This epileptic syndrome must be identified, and treated without delay. In fact, without appropriate treatment, the evolution may lead to a continuous spike-wave during the sleep with cognitive deterioration.
儿童期特发性加斯东枕叶癫痫是儿童特发性局灶性癫痫组中一种罕见但定义明确的综合征。临床表现以主要伴有视觉症状的简单部分性发作，随后继发全面性发作为特征。
报告一例儿童枕叶癫痫病例。
我们报告一例10岁女童，无既往病史。9岁时，患者开始出现无发热的重复性发作。首次发作包括几次伴有肌张力减退和发作后遗忘的意识丧失发作。第二种类型是在10分钟内出现三次刻板、复杂的视幻觉发作。一个月后，出现了第三种类型的强直阵挛性全面性发作。神经学检查和常规实验室检查均正常。脑部神经影像学检查正常。发作间期脑电图显示双侧慢波在过度换气时被激活。她接受了丙戊酸钠治疗。所有发作均停止，且未再发作。
必须及时识别并治疗这种癫痫综合征。事实上，若不进行适当治疗，病情进展可能导致睡眠期持续棘慢波发放并伴有认知功能恶化。
