马凡综合征自发性硬脑膜撕裂致颅内低血压和小脑扁桃体疝：病例报告。
Spontaneous dural tear leading to intracranial hypotension and tonsillar herniation in Marfan syndrome: a case report.
机构信息
Medical College, Aga Khan University Hospital, Stadium Road, P.O. Box 3500, Karachi, Pakistan.
出版信息
BMC Neurol. 2010 Jun 28;10:54. doi: 10.1186/1471-2377-10-54.
BACKGROUND
We describe the case of a 38 year old male with Marfan syndrome who presented with orthostatic headaches and seizures.
CASE PRESENTATION
The patient was diagnosed with Spontaneous Intracranial Hypotension secondary to CSF leaks, objectively demonstrated by MR myelogram with intrathecal contrast. Epidural autologous blood patch was administered at the leakage site leading to significant improvement.
CONCLUSION
Our literature search shows that this is the second reported case of a Marfan patient presenting with symptomatic spontaneous CSF leaks along with tonsillar herniation.
背景
我们描述了一例 38 岁男性马凡综合征患者，他表现为直立性头痛和癫痫发作。
病例介绍
患者被诊断为继发性自发性颅内低血压伴脑脊液漏，MR 脊髓造影显示椎管内有对比剂证实。在漏口处行硬膜外自体血贴治疗后，症状显著改善。
结论
我们的文献检索显示，这是第二例报告的马凡综合征患者出现症状性自发性脑脊液漏伴扁桃体疝的病例。
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