Mahore Amit, Chagla Aadil, Goel Atul
Department of Neurosurgery, Seth G.S. Medical College & King Edward VII Memorial Hospital, Parel, Mumbai, India.
J Korean Neurosurg Soc. 2010 Jun;47(6):454-7. doi: 10.3340/jkns.2010.47.6.454. Epub 2010 Jun 30.
Pure ventral midline giant schwannoma is an extremely rare entity. Spinal intradural extramedullary schwannomas commonly occur posterolateral or anterolateral to the spinal cord. A case of a pure midline ventrally situated giant pan cervical extramedullary schwannoma in an 18-year-old male patient with compressive myelopathy and sphincter involvement is presented. Spinal MR imaging showed a midline ventrally situated extramedullary tumor with severe spinal cord compression extending from clivus to C7 vertebra. It was resected through a posterolateral approach. Histology was consistent with a schwannoma. Post operative MR imaging showed no evidence of the tumor. The radiological features, pathogenesis and surgical strategies in management of these difficult tumors are discussed and the relevant literature is briefly reviewed.
纯腹侧中线巨大神经鞘瘤是一种极为罕见的疾病。脊髓硬膜内髓外神经鞘瘤通常发生于脊髓的后外侧或前外侧。本文报告一例18岁男性患者，患有纯中线腹侧位巨大全颈髓外神经鞘瘤，伴有压迫性脊髓病和括约肌受累。脊柱磁共振成像显示腹侧中线位髓外肿瘤，伴有严重脊髓压迫，范围从斜坡延伸至C7椎体。通过后外侧入路将其切除。组织学检查结果符合神经鞘瘤。术后磁共振成像显示无肿瘤迹象。本文讨论了这些疑难肿瘤的影像学特征、发病机制和手术策略，并简要回顾了相关文献。
