Jean Guillaume, Terrat Jean-Claude, Vanel Thierry, Hurot Jean-Marc, Lorriaux Christie, Mayor Brice, Chazot Charles
Centre de rein artificiel, 42, avenue du 8-mai-1945, 69160 Tassin La Demi-Lune, France.
Nephrol Ther. 2010 Nov;6(6):499-504. doi: 10.1016/j.nephro.2010.04.003. Epub 2010 Jun 2.
Calciphylaxis (CPX) or calcific uraemic arteriolopathy is a rare life-threatening complication, affecting mainly dialysis patients. The condition is characterized by calcifications and thrombosis of the small cutaneous vessels and small vessels in the fat tissue, resulting in the development of necrotizing and non-healing ulcers. The development of these lesions leads to poor outcomes owing to infectious complications and some frequently associated unfavourable medical conditions: obesity, diabetes, and peripheral vascular disease. We report the case of six patients with different clinical forms of CPX in the past 10 years with favourable outcomes observed in five of the six patients. The diagnosis was based on clinical presentation: bilateral and hyperalgesic necrotic lesions along with a history of mineral metabolism disorder or warfarin use. The therapeutic strategy included the following: daily dialysis, hyperbaric oxygen therapy, treatment of limb artery stenosis, maintenance of the optimal haemodynamic stability, delivery of cutaneous care, administration of analgesics and antibiotics, warfarin and calcium cessation, and additional therapy with cinacalcet or parathyroidectomy and therapy with bisphosphonates or sodium thiosulphate. Healing was observed in five out of six CPX patients by using this strategy that should be rapidly employed in order to decrease the necrotizing areas that result in poor outcomes. Prevention includes identification of at-risk patients in order to optimize the treatment of the identified risk factors for CPX.
钙化防御(CPX)或钙化性尿毒症小动脉病是一种罕见的危及生命的并发症,主要影响透析患者。该病的特征是皮肤小血管和脂肪组织中的小血管发生钙化和血栓形成,导致坏死性且不愈合溃疡的出现。这些病变的发展由于感染性并发症以及一些常见的不利医学状况(肥胖、糖尿病和外周血管疾病)而导致不良后果。我们报告了过去10年中6例不同临床形式CPX患者的病例,其中6例患者中有5例观察到了良好的结局。诊断基于临床表现:双侧且疼痛加剧的坏死性病变以及矿物质代谢紊乱或使用华法林的病史。治疗策略包括以下方面:每日透析、高压氧治疗、肢体动脉狭窄的治疗、维持最佳血流动力学稳定性、皮肤护理、给予镇痛药和抗生素、停用华法林和钙剂,以及使用西那卡塞或甲状旁腺切除术进行额外治疗,并用双膦酸盐或硫代硫酸钠进行治疗。通过使用该策略,6例CPX患者中有5例实现了愈合,应迅速采用该策略以减少导致不良后果的坏死区域。预防措施包括识别高危患者,以便优化对已确定的CPX危险因素的治疗。