Higuchi Mitsunori, Suzuki Hiroyuki, Shio Yutaka, Hoshi Sayuri, Gotoh Mitsukazu
Division of Thoracic Surgery, Department of Surgery 1, Fukushima Medical University School of Medicine, 1-Hikarigaoka, Fukushima 960-1295, Japan.
Gen Thorac Cardiovasc Surg. 2010 Jul;58(7):348-51. doi: 10.1007/s11748-009-0534-x. Epub 2010 Jul 14.
A low-grade fibromyxoid sarcoma (LGFMS), an Evans tumor, is highly unusual. It is rarely described as a primary neoplasm in the thoracic cavity. We experienced a case of a 20-year-old woman with a right intrathoracic tumor that was surgically treated. Postoperative pathology of the resected specimen revealed the tumor to be LGFMS based on its histological appearance, immunohistological staining, and evidence of fused in sarcoma (FUS) translocation by fluorescence in situ hybridization. Tumor resection was performed with a free surgical margin, and the resultant chest wall defect was repaired using prosthetic mesh. The patient has been well without any recurrence for 18 months since surgery.
低度纤维黏液样肉瘤（LGFMS），即埃文斯瘤，极为罕见。它很少被描述为胸腔原发性肿瘤。我们遇到一例20岁女性患有右胸内肿瘤并接受了手术治疗。切除标本的术后病理根据其组织学表现、免疫组织化学染色以及荧光原位杂交显示的肉瘤融合蛋白（FUS）易位证据，确定肿瘤为LGFMS。手术切缘阴性，使用人工补片修复了由此产生的胸壁缺损。自手术以来，患者状况良好，18个月未出现任何复发。
