Félix Lizarda, Souza Alex Rolland, Queiroz Ana Patrícia, Diniz Carolina, Lima Marcelo, Santos Roberta Espínola, Cardoso Alexandre S
Serviço de Ginecologia e Obstetrícia, Instituto Materno Infantil Prof. Fernando Figueira, Recife, Brasil.
Acta Med Port. 2010 May-Jun;23(3):505-10. Epub 2010 Jun 14.
Vein of Galen aneurysm is a rare congenital anomaly, originated from a defect in fusion of internal cerebral veins. Due to low resistance, it produces high debit cardiac insufficiency. It constitutes 1% of all intracranial vascular malformations. Prognosis depends on patient's age when the manifestation occurs and aneurysm size. The two reported cases are about fetal prenatal diagnosis of vein of Galen aneurysm, confirmed by ultrasonography, which evolved for caesarian delivery at term gestation. Magnetic resonance was carried out after birth, confirming prenatal diagnosis. The first patient had spontaneous thrombosis of the aneurysm while the second was submitted to embolization. Both of them had hospital discharge with ambulatory accompaniment. The prenatal ultrasonography diagnosis is fundamental to determine aneurysm size, defining the best treatment, when this procedure is indicated, and the more adequate obstetric and perinatal assistance.
大脑大静脉动脉瘤是一种罕见的先天性异常,起源于大脑内静脉融合缺陷。由于阻力低,它会导致高流量性心功能不全。它占所有颅内血管畸形的1%。预后取决于发病时患者的年龄和动脉瘤大小。报道的两例病例均为大脑大静脉动脉瘤的胎儿产前诊断,经超声检查确诊,足月妊娠时行剖宫产。出生后进行磁共振成像,证实产前诊断。第一例患者动脉瘤自发血栓形成,第二例接受了栓塞治疗。两人均在门诊陪同下出院。产前超声诊断对于确定动脉瘤大小、确定最佳治疗方案(如果有必要进行该手术)以及提供更适当的产科和围产期护理至关重要。