Adolf-Butenandt-Institute, Biochemistry, Ludwig-Maximilians-University, Munich, Germany.
EMBO J. 2010 Sep 1;29(17):3020-32. doi: 10.1038/emboj.2010.167. Epub 2010 Jul 30.
The amyloid precursor protein (APP) undergoes constitutive shedding by a protease activity called alpha-secretase. This is considered an important mechanism preventing the generation of the Alzheimer's disease amyloid-beta peptide (Abeta). alpha-Secretase appears to be a metalloprotease of the ADAM family, but its identity remains to be established. Using a novel alpha-secretase-cleavage site-specific antibody, we found that RNAi-mediated knockdown of ADAM10, but surprisingly not of ADAM9 or 17, completely suppressed APP alpha-secretase cleavage in different cell lines and in primary murine neurons. Other proteases were not able to compensate for this loss of alpha-cleavage. This finding was further confirmed by mass-spectrometric detection of APP-cleavage fragments. Surprisingly, in different cell lines, the reduction of alpha-secretase cleavage was not paralleled by a corresponding increase in the Abeta-generating beta-secretase cleavage, revealing that both proteases do not always compete for APP as a substrate. Instead, our data suggest a novel pathway for APP processing, in which ADAM10 can partially compete with gamma-secretase for the cleavage of a C-terminal APP fragment generated by beta-secretase. We conclude that ADAM10 is the physiologically relevant, constitutive alpha-secretase of APP.
淀粉样前体蛋白(APP)通过一种称为α-分泌酶的蛋白酶活性进行组成性脱落。这被认为是防止阿尔茨海默病淀粉样β肽(Abeta)生成的重要机制。α-分泌酶似乎是 ADAM 家族的一种金属蛋白酶,但它的身份仍有待确定。使用一种新型的α-分泌酶切割位点特异性抗体,我们发现 RNAi 介导的 ADAM10 敲低,但令人惊讶的是 ADAM9 或 17 的敲低,完全抑制了不同细胞系和原代小鼠神经元中 APP 的 α-分泌酶切割。其他蛋白酶无法弥补这种 α-切割的缺失。这一发现通过 APP 切割片段的质谱检测得到了进一步证实。令人惊讶的是,在不同的细胞系中,α-分泌酶切割的减少并没有伴随着 Abeta 生成的β-分泌酶切割的相应增加,这表明这两种蛋白酶并不总是将 APP 作为底物竞争。相反,我们的数据表明了 APP 加工的一种新途径,其中 ADAM10 可以部分与 γ-分泌酶竞争β-分泌酶生成的 APP C 端片段的切割。我们得出结论,ADAM10 是 APP 的生理相关的、组成性的α-分泌酶。