Bindal A K, Storrs B B, McLone D G
Division of Neurosurgery, Northwestern University Medical School, Children's Memorial Hospital, Chicago, Illinois.
Neurosurgery. 1991 Jun;28(6):844-7. doi: 10.1097/00006123-199106000-00009.
Occipital cephaloceles in the Dandy-Walker syndrome are not rare. To date, 28 cases have been reported. We report on 8 cases of associated occipital meningocele, totalling 16% of all patients with the Dandy-Walker syndrome in our series. In all patients, communication existed between the posterior fossa cyst and the occipital meningocele. In 2 patients, the occipital meningocele disappeared after cerebrospinal fluid shunting and never required surgical repair. It appears that the cranial defect had ossified and resulted in self-closure. Poor intellectual development in persons with the Dandy-Walker syndrome is associated with the presence of other central nervous system and systemic abnormalities and not with occipital meningoceles alone.
丹迪-沃克综合征中的枕部脑膨出并不罕见。迄今为止，已有28例相关报道。我们报告了8例合并枕部脑膜膨出的病例，占我们系列中所有丹迪-沃克综合征患者的16%。所有患者的后颅窝囊肿与枕部脑膜膨出之间均存在连通。2例患者在脑脊液分流后枕部脑膜膨出消失，且从未需要手术修复。似乎颅骨缺损已经骨化并导致自行闭合。丹迪-沃克综合征患者智力发育不良与其他中枢神经系统和全身异常有关，而不仅仅与枕部脑膜膨出有关。
