Shuto T, Sekido K, Ohtsubo Y, Saida A, Yamamoto I
Department of Neurosurgery, Kanagawa Children's Medical Center, Yokohama, Japan.
Neurol Med Chir (Tokyo). 1999 Jul;39(7):544-7. doi: 10.2176/nmc.39.544.
A neonate presented with Dandy-Walker syndrome associated with occipital meningocele and spinal lipoma, manifesting as soft masses on the skull and lumbosacral regions. Magnetic resonance imaging demonstrated a large posterior fossa cyst between the fourth ventricle and occipital meningocele, but the aqueduct was patent and there was no sign of hydrocephalus. A cyst-peritoneal shunt was emplaced at the age of 8 days followed by partial removal of the spinal lipoma and untethering of the cord at the 3 months. Follow-up examination of age 3 years found almost normal development, although the cyst still persisted.
