Rizvi Sadia, Mehboob Javed, Asghar Asghar H, Mateen Ahmed, Raza Tehseen, Hameed Abid
Department of Clinical Oncology, KIRAN Hospital, Karachi.
J Coll Physicians Surg Pak. 2010 Aug;20(8):554-5.
Malignant peripheral nerve sheath tumour (MPNST) is a very rare tumour with an incidence of one per 100,000 and constitutes between 3 to 10% of all soft tissue sarcomas. Most of the sarcoma involve the extremities and retroperitoneal regions. However, this case presented with mass in left inguinal region and then spread rapidly to omentum, assuming the appearance of an omental cake. Mass responded well to chemotherapy comprising of Ifosfamide and Doxorubicin.
恶性外周神经鞘瘤(MPNST)是一种非常罕见的肿瘤,发病率为十万分之一,占所有软组织肉瘤的3%至10%。大多数肉瘤累及四肢和腹膜后区域。然而,该病例表现为左腹股沟区肿块,随后迅速扩散至大网膜,呈大网膜饼状外观。肿块对由异环磷酰胺和阿霉素组成的化疗反应良好。