比尔斯-赫希特综合征与脉络膜新生血管形成。
Beals-Hecht syndrome and choroidal neovascularization.
作者信息
Gallego-Pinazo Roberto, López-Lizcano Ruth, Millán José María, Arevalo J Fernando, Mullor J Luis, Díaz-Llopis Manuel
机构信息
Department of Ophthalmology, University Hospital La Fe, Av Campanar, 21 46009,Valencia, Spain.
出版信息
Clin Ophthalmol. 2010 Aug 9;4:845-7. doi: 10.2147/opth.s11685.
PURPOSE
To describe a case of choroidal neovascularization (CNV) in a female diagnosed with Beals-Hecht syndrome.
METHODS
A retrospective, interventional case is described in a 26-year-old female complaining of metamorphopsia and visual loss in her left eye (counting fingers). The fluorescein angiogram and the optical coherence tomography supported the diagnosis of CNV. Intravitreal ranibizumab was administered.
RESULTS
After the third intravitreal ranibizumab, her visual acuity improved to 0.8 and the morphology of the macular area was restored.
CONCLUSIONS
To our knowledge this is the first report of CNV in Beals-Hecht syndrome treated with ranibizumab. Self-monitoring by periodically performing Amsler grid test is strongly recommended in these patients in order to achieve an early diagnosis of eventual CNV and avoid visual acuity loss.
目的
描述一例被诊断为贝氏-赫氏综合征的女性脉络膜新生血管（CNV）病例。
方法
对一名26岁女性进行回顾性、介入性病例描述，该女性主诉左眼视物变形及视力丧失（仅能数指）。荧光素血管造影和光学相干断层扫描支持CNV的诊断。给予玻璃体内注射雷珠单抗。
结果
在第三次玻璃体内注射雷珠单抗后，她的视力提高到0.8，黄斑区形态恢复。
结论
据我们所知，这是首例使用雷珠单抗治疗贝氏-赫氏综合征合并CNV的报告。强烈建议这些患者定期进行阿姆斯勒方格表测试进行自我监测，以便早期诊断可能出现的CNV并避免视力丧失。
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