Kulenkampff H A, Richter G M, Hasse W E, Adler C P
Orthopädische Abteilung, Universitätskliniken, Freiburg, Federal Republic of Germany.
Int Orthop. 1990;14(4):361-6. doi: 10.1007/BF00182645.
Massive osteolysis is a very rare tumour-like lesion usually affecting young adults. There are 132 reported cases which we have reviewed, including 31 single cases of pelvic involvement. The term "massive osteolysis" is based on the typical radiological findings, such as increasing translucency and loss of bone density. The diagnosis of the Gorham-Stout syndrome must be confirmed by the microscopic finding of intramedullary vascular structures. Our patient was a 23 year old white Caucasian, who had the full clinical signs of Gorham-Stout syndrome. She had achieved 2 normal pregnancies and deliveries in spite of her massive pelvic osteolysis.
巨大骨溶解是一种非常罕见的肿瘤样病变，通常影响年轻人。我们回顾了132例已报道的病例，其中包括31例骨盆受累的单发病例。“巨大骨溶解”这一术语基于典型的放射学表现，如透亮度增加和骨密度丧失。戈勒姆-斯托特综合征的诊断必须通过骨髓血管结构的显微镜检查结果来证实。我们的患者是一名23岁的白种女性，具有戈勒姆-斯托特综合征的全部临床体征。尽管她患有巨大的骨盆骨溶解，但她已成功经历了2次正常妊娠和分娩。
