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成年难治性室性心动过速患者巨大左心室壁内纤维瘤的外科治疗

Surgical treatment of giant intramural left ventricular fibroma in an adult patient with refractory ventricular tachycardia.

作者信息

Gualis Javier, Castaño Mario, Gómez-Plana Jesús, Martín Carlos, Alonso David

机构信息

Department of Cardiac Surgery, Hospital de León, León, Spain.

出版信息

J Card Surg. 2010 Nov;25(6):656-8. doi: 10.1111/j.1540-8191.2010.01105.x. Epub 2010 Aug 27.

Abstract

Cardiac fibromas are rare benign tumors predominantly diagnosed in children and teenagers. We report a 57-year-old male patient with class II dyspnea and angina. During electrocardiographic assessment, recurrent ventricular tachycardia was present and magnetic resonance imaging revealed a giant (12.5 × 5 × 4 cm) intramural left ventricular tumor compatible with cardiac fibroma. After surgical biopsy and histological confirmation, open-heart surgical resection was successfully performed. After nine months of follow up, the patient remains asymptomatic without evidence of ventricular tachycardia.

摘要

心脏纤维瘤是罕见的良性肿瘤,主要在儿童和青少年中被诊断出来。我们报告一例57岁男性患者,有II级呼吸困难和心绞痛症状。在心电图评估期间,发现有反复发作的室性心动过速,磁共振成像显示左心室壁内有一个巨大的(12.5×5×4厘米)肿瘤,符合心脏纤维瘤的表现。经过手术活检和组织学确认后,成功进行了心脏直视手术切除。经过九个月的随访,患者仍无症状,未出现室性心动过速迹象。

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