Martini B, Bassan L, Della Valentina P, Valente M, Buja G F
Cattedra di Cardiologia, Università di Padova.
Minerva Cardioangiol. 1990 Jul-Aug;38(7-8):345-7.
B.P., asymptomatic until her fifties, was admitted to hospital because of precordial pain. Her ECG and chest X rays were normal. When 52 she was again admitted, because of congestive heart failure. ECG showed repolarization abnormalities and chest X rays showed marked cardiomegaly. 2d echocardiogram was consistent with right atrial dilatation, dislodged posterior leaflet of the tricuspid valve and marked tricuspid regurgitation; these features were consistent with Ebstein anomaly. The patient was successfully treated by digitalis and diuretics. This case shows that in very rare cases this congenital heart disease can produce its clinical manifestations only late in lifetime.
B.P. 在五十多岁之前没有症状，因心前区疼痛入院。她的心电图和胸部X光片正常。52岁时，她因充血性心力衰竭再次入院。心电图显示复极异常，胸部X光片显示明显的心脏扩大。二维超声心动图显示右心房扩张、三尖瓣后叶脱垂和明显的三尖瓣反流；这些特征与埃布斯坦畸形一致。该患者通过洋地黄和利尿剂成功治疗。该病例表明，在极少数情况下，这种先天性心脏病仅在生命后期才出现临床表现。
