Starcevic Mirta, Sepec Marija Pozgaj, Zah Vanja
Department of Pediatrics, Sestre Milosrdnice University Hospital Zagreb, Zagreb, Croatia.
Pediatr Dermatol. 2010 Sep-Oct;27(5):540-2. doi: 10.1111/j.1525-1470.2010.01266.x. Epub 2010 Aug 27.
Aplasia cutis congenita is a rare, sporadic congenital malformation characterized by skin defects, sometimes extending to the underlying bone. We report a case of a boy born with a large rhomboid scalp and skull defect measuring 8 × 12 cm with no other anomalies. Conservative treatment led to the complete epithelization of the skin defect with secondary closure of the cranial vault without need for surgical intervention.
先天性皮肤发育不全是一种罕见的散发性先天性畸形,其特征为皮肤缺损,有时可延伸至深部骨骼。我们报告一例男婴,出生时即有一个8×12厘米的巨大菱形头皮和颅骨缺损,无其他异常。保守治疗使皮肤缺损完全上皮化,颅顶继发闭合,无需手术干预。