Hamdan Mohamed A, Begam Muzibunnisa, Mirghani Hisham M
Department of Pediatrics, Tawam Hospital, Al Ain, United Arab Emirates.
Pediatr Cardiol. 2010 Nov;31(8):1252-3. doi: 10.1007/s00246-010-9784-8. Epub 2010 Sep 8.
Conjoined twins occur at the rate of 1 in 50 to 200,000 live births, and 75% of these share the thorax (thoracopagus) or the thorax and upper abdomen (thoraco-omphalopagus), resulting in cardiac and hepatic sharing. Antenatal diagnosis can delineate the cardiac anatomy and provide parental counseling on whether separation is possible after birth. In the majority of cases, thoracopagus twins have a complex cardiac anatomy and share a common pericardial sac. Separation and survival depend on the extent to which the cardiac chambers and conduction system are fused. When the twins share the atria, ventricles, or both, death is inevitable even if surgical separation is occasionally attempted.
联体双胎的发生率为每50至20万例活产中有1例,其中75%的联体双胎共用胸部(胸部联体双胎)或胸部和上腹部(胸腹联体双胎),导致心脏和肝脏共用。产前诊断可以明确心脏解剖结构,并为父母提供关于出生后是否可以分离的咨询。在大多数情况下,胸部联体双胎具有复杂的心脏解剖结构,并共用一个心包腔。分离和存活取决于心脏腔室和传导系统融合的程度。当双胎共用心房、心室或两者时,即使偶尔尝试手术分离,死亡也不可避免。