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血小板无力症与妊娠

Glanzmann's thrombasthenia and pregnancy.

作者信息

Walters J P, Hall J S

机构信息

Department of Pathology, U.W.I., Jamaica.

出版信息

West Indian Med J. 1990 Dec;39(4):256-8.

PMID:2082573
Abstract

Glanzmann's thrombasthenia is a rare congenital disorder of platelet function manifesting as defective primary haemostasis. Bleeding episodes often require platelet transfusions, and allo-immunization to donor platelets may occur. The problems of ensuring adequate haemostatic potential for delivery of an allo-immunized pregnant female with Glanzmann's thrombasthenia are presented.

摘要

血小板无力症是一种罕见的先天性血小板功能障碍,表现为原发性止血缺陷。出血发作常常需要输注血小板,并且可能会发生对供体血小板的同种免疫。本文介绍了为一名患有血小板无力症且发生同种免疫的妊娠女性提供足够止血潜能时所面临的问题。

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