Uchida Daisuke, Ogawa Tsuneyoshi, Ueki Toru, Kominami Yoko, Numata Norifumi, Matsusita Hiroshi, Morimoto Yuki, Nakarai Asuka, Ota Shigeru, Nanba Shintaro, Takada Shinichi, Iwado Shota, Kurome Manabu, Ohe Hirotoki, Okamoto Ryoichi, Uematsu Syuji, Nakagawa Masahiro, Ishida Kiyotaka, Araki Yasuyuki, Mizuno Motowo
Department of Internal Medicine, Hiroshima City Hospital, Hiroshima, Japan.
Nihon Shokakibyo Gakkai Zasshi. 2010 Sep;107(9):1456-65.
We report a 67-year-old woman who had stiff shoulders and anemia. Upper gastrointestinal endoscopy revealed a pedunclated nodular submucosal tumor with erosions and surface ulcers in the second portion of the duodenum. These endoscopic findings were thought to be characteristic of gangliocytic paraganglioma. CT scan revealed suspected lymph node metastasis, thus the tumor was resected with pancreaticoduodenectomy and was found to be a gangliocytic paraganglioma associated with lymph nodal metastasis. Due to the rarity of the disease there is no consensus regarding treatment. Although this tumor is considered benign, the possibility exists for regional lymph nodal spread. The treatment should be well planned with continuous careful evaluation.
我们报告了一位67岁患有肩部僵硬和贫血的女性。上消化道内镜检查显示十二指肠第二部有一个带蒂的结节状黏膜下肿瘤，伴有糜烂和表面溃疡。这些内镜检查结果被认为是神经节细胞性副神经节瘤的特征。CT扫描显示怀疑有淋巴结转移，因此该肿瘤通过胰十二指肠切除术切除，结果发现是一个伴有淋巴结转移的神经节细胞性副神经节瘤。由于该疾病罕见，关于治疗尚无共识。尽管这种肿瘤被认为是良性的，但仍存在区域淋巴结扩散的可能性。治疗应精心规划并持续进行仔细评估。
