Department of Medicine, Surgery and Dentistry, Division of Pathology, AO S, Paolo e Fondazione IRCCS Ospedale Maggiore Policlinico, Mangiagalli and Regina Elena, University of Milan Medical School, Milan, Italy.
BMC Gastroenterol. 2010 Sep 14;10:105. doi: 10.1186/1471-230X-10-105.
Few cases of primary retroperitoneal mucinous cystoadenoma, a rare benign tumor, have been reported in the literature so far. The pathogenesis of this tumour is not completely understood yet.Our case is particularly significant since the localization in the mesentery has been described only once before in the literature. Unless biologically benign, this tumour can cause relevant clinical symptoms related to the size and site (compression or obstruction of organs).
We describe the case of a 52-years old woman who had presented with abdominal pain and underwent surgery in order to remove a palpable lump in the mesentery with histological diagnosis of primary mucinous cystoadenoma. The patient was followed-up for two years with no evidence of recurrence.
Mucinous cystoadenoma is more frequent in women, particularly when there is history of one or more pregnancies. A complete preoperative study with abdominal and pelvic tomographic images and an accurate physical examination are essentials for the management of the patient. Surgical resection is the only way to treat mucinous cystoadenomas, and to have the histological confirmation that the removed mass is a benign tumor.
原发性腹膜后黏液囊腺瘤是一种罕见的良性肿瘤，目前文献中报道的病例很少。该肿瘤的发病机制尚未完全阐明。我们的病例尤为重要，因为其在肠系膜的定位仅在文献中描述过一次。除非生物学上为良性，否则该肿瘤可能会引起与大小和部位相关的相关临床症状（器官压迫或梗阻）。
我们描述了一位 52 岁女性的病例，她因腹痛就诊，并接受了手术，以切除肠系膜上可触及的肿块，组织学诊断为原发性黏液囊腺瘤。该患者在两年内进行了随访，无复发迹象。
黏液囊腺瘤在女性中更为常见，尤其是有一次或多次妊娠史的女性。全面的术前研究，包括腹部和盆腔的断层图像和准确的体格检查，是患者管理的关键。手术切除是治疗黏液囊腺瘤的唯一方法，并可通过组织学确认切除的肿块为良性肿瘤。
