Bouvet J P, Leveque D, Bernetieres F, Gros J J
Eur J Pediatr. 1978 May 22;128(1):17-26. doi: 10.1007/BF00496922.
Vascularization of the arms has been studied by impedance plethysmography (rheography) in eight children with Poland syndrome, a common malformation characterized by unilateral hand anomaly and ipsilateral aplasia of the inferior head of the pectoralis major muscle. A marked decrease of the velocity of the systolic increase in the arterial volume (Velm) was shown in the affected arms, and the difference between the two arms was significantly higher in the patients than in a control group (P less than 0.02). These results, which are also observed in stenotic atherosclerosis, support the hypothesis of hypoplasia of the ipsilateral subclavian artery as the origin of the malformation, although a local anomaly in arterial-wall viscosity cannot be ruled out. The opacification of the aortic arch in another patient confirmed this hypothesis. Aortography in further patients will be necessary to substantiate our results. However, this technique is not without danger and should only be used during the first months of life when a vascular operation can be envisaged.
采用阻抗体积描记法（血流描记法）对8例患有波兰综合征的儿童的手臂血管形成情况进行了研究。波兰综合征是一种常见的畸形，其特征为单侧手部异常以及同侧胸大肌下头发育不全。结果显示，患侧手臂动脉血容量收缩期增加速度（Velm）显著降低，且患者双臂之间的差异明显高于对照组（P<0.02）。在动脉粥样硬化狭窄病例中也观察到了这些结果，这支持了同侧锁骨下动脉发育不全是该畸形起源的假说，不过不能排除动脉壁黏度存在局部异常的可能性。另一例患者的主动脉弓显影证实了这一假说。有必要对更多患者进行主动脉造影以证实我们的结果。然而，这项技术并非毫无风险，仅应在考虑进行血管手术的生命最初几个月使用。
