Morales Olga Lucía, Valencia María de la Luz, Gómez Carolina, Pérez María del Pilar, Sanín Emilio, Vásquez Luz Marina
Sección de Neumología Pediátrica, Grupo Pediaciencias, Departamento de Pediatría, Facultad de Medicina, Universidad de Antioquia, Medellín, Colombia.
Biomedica. 2010 Jan-Mar;30(1):10-4.
Chest wall mesenchymal hamartoma is an extremely rare benign tumor. Approximately 80 cases have been reported in the literature. Most tumors are manifested at birth with a painless palpable mass of the chest wall, usually unilateral. Respiratory symptoms result from extrinsic compression of the pulmonary parenchyma, and the severity of the symptoms will depend on the size and location of the lesion. Imaging features are characteristic, but definitive diagnosis is histological. Herein, a case is described of a four month old infant with diagnosis of chest wall mesenchymal hamartoma, manifested at birth. Different treatment options are described, including expectations from tumor management, the possibility of spontaneous regression, and the morbidity associated with the surgical option.
胸壁间叶性错构瘤是一种极其罕见的良性肿瘤。文献报道约80例。大多数肿瘤在出生时表现为胸壁可触及的无痛肿块，通常为单侧。呼吸症状是由于肺实质受到外部压迫所致，症状的严重程度取决于病变的大小和位置。影像学特征具有特异性，但确诊需依靠组织学检查。本文描述了一例出生时即被诊断为胸壁间叶性错构瘤的4个月大婴儿病例。文中还介绍了不同的治疗方案，包括对肿瘤治疗的预期、自发消退的可能性以及手术治疗相关的发病率。
