Pozdnikin Iu I, Ryzhakov Iu P
Ortop Travmatol Protez. 1990 Nov(11):5-10.
In the article are presented the results of observation of 8 patients, aged 4-16 years, with Ehlers-Danlos++ syndrome, one of the most frequent hereditary disease with generalized affection of connective tissue. ++Clinico-roentgenologic characteristic of kyphotic-scoliotic++ deformity of vertebral column indicates its progressive nature, that determines indications for surgical intervention but concomitant changes of cardiovascular system should be considered. Preoperative preparation includes measures for vertebral column mobilization as well as pharmacotherapy with retabolil in combination with ascorbic acid, calcetrine and methyluracil++. Selected method of operative treatment is Harrington-Luck techniques in case of scoliosis prevalence and application of original endocorrector with associated influence at kyphotic component. As a result of treatment scoliosis is corrected, on average, by 49,2% and kyphosis by 62,7%.
本文介绍了对8例4至16岁患有埃勒斯-当洛++综合征患者的观察结果，该综合征是最常见的遗传性疾病之一，会导致结缔组织全身性受累。++脊柱后凸-脊柱侧凸畸形的临床-放射学特征表明其具有进行性，这决定了手术干预的指征，但应考虑心血管系统的伴随变化。术前准备包括脊柱松动措施以及使用去氢甲睾酮联合抗坏血酸、钙三醇和甲基尿嘧啶进行药物治疗。++在脊柱侧凸占主导的情况下，选择的手术治疗方法是哈林顿-勒克技术，并应用对后凸成分有相关影响的原创内固定器。治疗结果显示，脊柱侧凸平均矫正49.2%，后凸矫正62.7%。
