Mentzel T, Kutzner H, Requena L, Hartmann A
Dermatopathologie, Friedrichshafen, Siemensstr. 6/1, 88048, Friedrichshafen.
Pathologe. 2010 Oct;31(6):489-96. doi: 10.1007/s00292-010-1361-7.
A number of hereditary tumor syndromes are associated with characteristic dermal neoplasms and knowledge and early diagnosis of these lesions may facilitate the diagnostic of the underlying syndrome. These syndromes include Muir-Torre syndrome, associated with cystic sebaceomas, Cowden syndrome, associated with multiple tricholemmomas, Carney complex associated with multiple superficial angiomyxomas, Birt-Hogg-Dubé syndrome associated with multiple fibrofolliculomas, tuberous sclerosis associated with multiple facial angiofibromas and so-called Koenen tumors, patients with renal cell cancer associated with pilar leiomyomatosis and uterine leiomyomas, Gardner syndrome associated with Gardner fibromas and nevoid basal cell carcinoma associated with multiple basal cell carcinomas in young patients.
许多遗传性肿瘤综合征与特征性皮肤肿瘤相关,了解这些病变并早期诊断可能有助于诊断潜在的综合征。这些综合征包括与囊性皮脂腺瘤相关的穆尔-托雷综合征、与多发性毛发上皮瘤相关的考登综合征、与多发性浅表血管黏液瘤相关的卡尼综合征、与多发性纤维毛囊瘤相关的伯-霍-杜综合征、与多发性面部血管纤维瘤和所谓的科嫩瘤相关的结节性硬化症、与毛囊平滑肌瘤病和子宫平滑肌瘤相关的肾细胞癌患者、与加德纳纤维瘤相关的加德纳综合征以及与年轻患者多发性基底细胞癌相关的痣样基底细胞癌综合征。