Department of Pathology, 251th Hospital of PLA, Zhang jiakou 075000, China.
Ann Diagn Pathol. 2011 Dec;15(6):427-30. doi: 10.1016/j.anndiagpath.2010.07.006. Epub 2010 Oct 30.
The perivascular epithelioid cell family of tumors includes angiomyolipoma, clear cell "sugar" tumor of the lung, lymphangioleiomyomatosis, and clear cell myomelanocytic tumor of the falciform ligament/ligamentum teres. Less frequently, perivascular epithelioid cell tumors arise in various other locations throughout the body including soft tissue, bone, and visceral organs. We report a case of a 23-year-old man who presented with 2-month history of frequent micturition and odynuria. Based on clinical examination, ultrasound computed tomography imaging, surgical operation, and histopathologic studies, a definitive diagnosis was made. Further characteristic images and pathology of this disease are discussed.
血管周上皮样细胞肿瘤家族包括血管平滑肌脂肪瘤、肺透明细胞“糖”瘤、淋巴管平滑肌瘤病和镰状韧带/蒂状韧带的透明细胞肌黑色素细胞瘤。较少见的是，血管周上皮样细胞肿瘤也可发生于身体的其他各种部位，包括软组织、骨和内脏器官。我们报告 1 例 23 岁男性，其主要表现为 2 个月的尿频和尿痛病史。根据临床检查、超声计算机断层扫描成像、手术操作和组织病理学研究，做出了明确诊断。进一步讨论了该病的特征性图像和病理学。
