Department of Urology, Peking Union Medical College Hospital, Peking Union Medical College, Chinese Academy of Medical Sciences, Beijing 100730, China.
Ir J Med Sci. 2011 Jun;180(2):557-60. doi: 10.1007/s11845-010-0616-x. Epub 2010 Nov 2.
Epithelioid angiomyolipoma (eAMLoma) is an uncommon renal mesenchymal tumor with malignant potential. It is composed of tumor cells arranged in an epithelioid manner. Differential diagnosis from renal cell carcinoma is often challenging because of its epithelioid morphology. Herein is reported a case of eAMLoma, involving a 49-year-old man with eAMLoma. The patient had undergone radical nephrectomy via retroperitoneal laparoscope successfully. He had an uneventful postoperative recovery. The tumor was positive for Desmin, Hmb45, and Sma. We recommend surgical treatment and a follow-up regimen similar to that for renal carcinoma. There was no recurrence and metastases after 1-year follow-up.
上皮样血管平滑肌脂肪瘤(eAMLoma)是一种罕见的具有恶性潜能的肾间叶性肿瘤。它由排列成上皮样的肿瘤细胞组成。由于其上皮样形态,与肾细胞癌的鉴别诊断常常具有挑战性。本文报告了一例 eAMLoma 病例,涉及一名 49 岁男性患者。该患者通过腹膜后腹腔镜成功进行了根治性肾切除术。术后恢复顺利。肿瘤免疫组化结果显示 Desmin、Hmb45 和 Sma 阳性。我们建议采用与肾细胞癌相似的手术治疗和随访方案。患者在 1 年随访期间未出现复发和转移。