Chen Jimei, Zhou Chengbin, Zhuang Jian
Department of Cardiovascular Surgery, Guangdong Provincial Cardiovascular Institute, Guangdong General Hospital, Guangdong Academy of Medical Sciences, 96 Dongchuan Road, Guangzhou 510080, China.
Pediatr Cardiol. 2011 Jan;32(1):78-80. doi: 10.1007/s00246-010-9800-z. Epub 2010 Nov 4.
Transposition of the great arteries with a ventricular septal defect and an associated aortopulmonary window is a rare anatomic combination having a high risk for pulmonary hypertension. Arterial switch with closure of the ventricular septal defect and repair of the aortopulmonary window is the procedure of choice, but a postoperative pulmonary hypertensive crisis is a common occurrence associated with significant morbidity and mortality. This report describes one case of such an anatomic lesion, which was repaired successfully with a fenestrated ventricular septal defect patch as an adjunct to decrease the risk of a postoperative pulmonary hypertensive crisis.
大动脉转位合并室间隔缺损及相关主肺动脉窗是一种罕见的解剖学组合，发生肺动脉高压的风险很高。动脉调转术联合室间隔缺损修补及主肺动脉窗修复是首选术式，但术后肺动脉高压危象很常见，会导致显著的发病率和死亡率。本报告描述了1例此类解剖学病变，通过使用带孔室间隔缺损补片作为辅助手段成功修复，以降低术后肺动脉高压危象的风险。
