Division of Vascular and Endovascular Surgery, Department ofSurgery, University of Arizona, USA.
J Vasc Surg. 2011 Feb;53(2):478-82. doi: 10.1016/j.jvs.2010.08.076. Epub 2010 Nov 3.
Marfan syndrome is an autosomally inherited disorder affecting the synthesis of connective tissues. Vascular manifestations of Marfan syndrome include aneurysmal dilatation of the aortic root, aortic dissection, and rupture. Peripheral aneurysms are mostly reported in the iliac, femoral, and subclavian arteries. We report a Marfan patient with a ruptured axillary artery aneurysm and a large left internal mammary artery aneurysm. The axillary aneurysm was successfully excluded using covered stent grafts, and the left internal mammary artery aneurysm was effectively coiled. Duplex ultrasound imaging at 4 months and computed tomography at 9 months demonstrated complete thrombosis and exclusion of both aneurysms with patent subclavian-axillary stent grafts.
马凡综合征是一种常染色体遗传性疾病,影响结缔组织的合成。马凡综合征的血管表现包括主动脉根部的瘤样扩张、主动脉夹层和破裂。周围动脉瘤主要发生在髂动脉、股动脉和锁骨下动脉。我们报告了一例马凡综合征患者,其患有破裂的腋动脉动脉瘤和巨大的左内乳动脉动脉瘤。腋动脉动脉瘤成功地用覆膜支架进行了排除,左内乳动脉动脉瘤则有效地进行了弹簧圈栓塞。4 个月时的双功能超声成像和 9 个月时的计算机断层扫描显示,两个动脉瘤均完全血栓形成并排除,锁骨下-腋动脉支架通畅。