Szturmowicz Monika, Wilińska Ewelina, Paczek Anna, Wawrzyńska Liliana, Opoka Lucyna, Gątarek Juliusz, Langfort Renata, Rowińska-Zakrzewska Ewa, Torbicki Adam
Department of Chest Medicine, National Tuberculosis and Lund Diseases Research Institute, Warsaw, Poland.
Pneumonol Alergol Pol. 2010;78(6):445-50.
Primary Sjögren's Syndrome (pSS) is a chronic, slowly progressive inflammatory autoimmune disorder, characterised by lymphocytic infiltration of the exocrine glands, leading to decrease of glandular secretion. In 40-60% of pSS patients, extraglandular disease develops. We present the case of a patient with two extraglandular sites involvement in the course of pSS manifesting with progressive respiratory and gastrointestinal symptoms.
原发性干燥综合征(pSS)是一种慢性、渐进性炎症性自身免疫性疾病,其特征是外分泌腺淋巴细胞浸润,导致腺体分泌减少。40%-60%的pSS患者会出现腺体外疾病。我们报告了一例在pSS病程中出现两个腺体外部位受累的患者,表现为进行性呼吸和胃肠道症状。