Farley-Loftus Rachel, Mandal Rajni, Latkowski Jo-Ann
Department of Dermatology, New York University, New York, NY, USA.
Dermatol Online J. 2010 Nov 15;16(11):8.
Poikilodermatous mycosis fungoides is a rare form of cutaneous T-cell lymphoma that is characterized clinically by localized or diffuse patches, which consist of telangiectases, mottled hyper- and hypopigmentation, and atrophy. The immunophenotype of neoplastic cells is similar to that observed in classic mycosis fungoides. Therapeutic options used in poikilodermatous and classic mycosis fungoides include both skin-directed and systemic treatments. We present a case of poikilodermatous mycosis fungoides in a 53-year-old woman, who initially presented with erythroderma and who has failed multiple treatment modalities.
色素沉着性蕈样肉芽肿是一种罕见的皮肤T细胞淋巴瘤，临床上以局限性或弥漫性斑块为特征，这些斑块由毛细血管扩张、斑驳状色素沉着和色素减退以及萎缩组成。肿瘤细胞的免疫表型与经典蕈样肉芽肿中观察到的相似。色素沉着性和经典蕈样肉芽肿的治疗选择包括皮肤定向治疗和全身治疗。我们报告一例53岁女性色素沉着性蕈样肉芽肿病例，该患者最初表现为红皮病，并且多种治疗方式均失败。
