Na Woon Tae, Lee Tae Hee, Lee Byung Seok, Kim Seok Hyun, Chae Hee Bok, Kim Seok Bae, Kim Yong Seok, Kim Sun Moon, Im Euyi Hyeog, Huh Kyu Chan, Choi Young Woo, Kang Young Woo
Department of Internal Medicine, Konyang University College of Medicine, Daejeon, Korea.
Korean J Gastroenterol. 2010 Dec;56(6):353-8. doi: 10.4166/kjg.2010.56.6.353.
BACKGROUND/AIMS: cystic lymphangioma is an uncommon disease, and rarely develops in the intraabdomen. The aim of this article was to discuss about clinical characteristics of intraabdominal cystic lymphangioma developed in Korea.
age, sex, symptoms, locations and size of the lesions, diagnostic methods, treatments, complications and recurrence were analyzed in 13 pathologically confirmed cases of intraabdominal cystic lymphangioma and 18 cases of literature consideration reported in Korea.
intraabdominal cystic lymphangioma commonly developed in adults compared to the other lymphangioma, and frequently located in the mesentery. Abdominal pain was the most common symptom, but it was a non-specific finding. Tenderness and abdominal mass were not significantly associated. The size of mass was diverse. Abdominal ultrasonography and abdominal CT were diagnostic tools most commonly used, but preoperative diagnosis was possible only in 22.6%. All patients were discharged without any complications, and no recurrence was reported.
preoperative diagnosis of intraabdominal cystic lymphangioma is difficult and symptoms and signs are not specific. Intraabdominal cystic lymphangioma should be suspected in patients with non specific abdominal pain and intraabdominal mass and active diagnostic evaluation is mandatory.
背景/目的：囊性淋巴管瘤是一种罕见疾病，很少发生于腹腔内。本文旨在探讨韩国发生的腹腔内囊性淋巴管瘤的临床特征。
对13例经病理证实的腹腔内囊性淋巴管瘤病例以及韩国报道的18例文献病例的年龄、性别、症状、病变部位和大小、诊断方法、治疗、并发症及复发情况进行分析。
与其他淋巴管瘤相比，腹腔内囊性淋巴管瘤常见于成人，且常位于肠系膜。腹痛是最常见症状，但为非特异性表现。压痛与腹部肿块无明显关联。肿块大小不一。腹部超声和腹部CT是最常用的诊断工具，但术前仅22.6%的病例能够确诊。所有患者均无并发症出院，且无复发报道。
腹腔内囊性淋巴管瘤术前诊断困难，症状和体征不具特异性。对于有非特异性腹痛和腹腔内肿块的患者应怀疑腹腔内囊性淋巴管瘤，必须积极进行诊断评估。
