Wiatr E, Kamiński Z, Pirozyński M, Szymczyk E
III Kliniki Gruźlicy i Chorób Płuc, Warszawie.
Pneumonol Pol. 1990 Apr-May;58(4-5):223-7.
A case of Wegener's granulomatosis in a 54 year old female is presented. The disease course was fulminating, the necrotic process involving lungs, gingiva, skin, trachea, producing finally a tracheo-esophageal fistula. Therapy with cyclophosphamide and prednisone produced resolution of all organ involvement except for the tracheo-esophageal fistula.
本文报告一例54岁女性的韦格纳肉芽肿病。病程呈暴发性,坏死过程累及肺、牙龈、皮肤、气管,最终形成气管食管瘘。环磷酰胺和泼尼松治疗使除气管食管瘘外的所有器官受累情况均得到缓解。