Criscione Vincent, Lachiewicz Anne, Robinson-Bostom Leslie, Grenier Nicole, Dill Sara Worthing
Department of Dermatology, Rhode Island Hospital, The Warren Alpert Medical School of Brown University, Providence, Rhode Island 02903, USA.
Pediatr Dermatol. 2010 Sep-Oct;27(5):514-7. doi: 10.1111/j.1525-1470.2010.01272.x.
Porokeratotic eccrine ostial and dermal duct nevus is a rare hamartomatous malformation, histologically characterized by cornoid lamellae overlying dilated eccrine ostia. The nevus most commonly presents in the form of multiple filiform keratotic spines in a linear arrangement, usually on the distal extremities. Porokeratotic eccrine and hair follicle nevus is thought to be a variant of porokeratotic eccrine ostial and dermal duct nevus that additionally involves hair follicle infundibula. We report a case of widespread Porokeratotic eccrine and hair follicle nevus that developed in a 15-year-old woman with keratitis-ichthyosis-deafness syndrome.
汗孔角化性小汗腺开口和真皮导管痣是一种罕见的错构瘤性畸形，组织学特征为扩张的小汗腺开口上方有鸡眼样板层。该痣最常见的表现形式是多个丝状角化性棘突呈线性排列，通常位于远端肢体。汗孔角化性小汗腺和毛囊痣被认为是汗孔角化性小汗腺开口和真皮导管痣的一种变体，其额外累及毛囊漏斗部。我们报告一例广泛分布的汗孔角化性小汗腺和毛囊痣，发生于一名患有角膜炎-鱼鳞病-耳聋综合征的15岁女性。
