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采用部分胸骨切开术和胸骨-肋软骨成形术的开放入路治疗合并漏斗胸的主动脉瓣环扩张症。

Open door approach by partial sternotomy and sterno-costo-chondroplasty for annuloaortic ectasia with pectus excavatum.

作者信息

Kawamura Tomonori, Fukuda Ikuo, Minakawa Masahito, Fukui Kozo

机构信息

Department of Thoracic and Cardiovascular Surgery, Hirosaki University Graduate School of Medicine, 5 Zaifu-cho, Hirosaki, Aomori 036-8562, Japan.

出版信息

Interact Cardiovasc Thorac Surg. 2011 Apr;12(4):645-7. doi: 10.1510/icvts.2010.258368. Epub 2011 Jan 25.

DOI:10.1510/icvts.2010.258368
PMID:21266492
Abstract

A 32-year-old female patient with Marfan syndrome was admitted for repair of annuloaortic ectasia and severe pectus excavatum. Because the chest cage deformity was severe, concomitant reparative surgery of the chest wall was performed. Partial median sternotomy and left second-fifth rib division was made to obtain good surgical field. The patient underwent valve-sparing aortic root remodeling successfully. After complete neutralization of heparin, additional division of the right ribs was performed and each rib and the sternum was reshaped. Pectus excavatum was completely repaired by this method. We believe this approach is efficacious for intracardiac repair with severe pectus excavatum.

摘要

一名32岁患有马凡综合征的女性患者因主动脉环扩张和严重漏斗胸修复入院。由于胸廓畸形严重,同时进行了胸壁修复手术。采用部分正中胸骨切开术和左第二至五肋分开术以获得良好的手术视野。患者成功接受了保留瓣膜的主动脉根部重塑手术。在肝素完全中和后,进行了右肋额外分开术,并对每根肋骨和胸骨进行了重塑。漏斗胸通过这种方法得到了完全修复。我们认为这种方法对于伴有严重漏斗胸的心脏内修复是有效的。

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1
Open door approach by partial sternotomy and sterno-costo-chondroplasty for annuloaortic ectasia with pectus excavatum.采用部分胸骨切开术和胸骨-肋软骨成形术的开放入路治疗合并漏斗胸的主动脉瓣环扩张症。
Interact Cardiovasc Thorac Surg. 2011 Apr;12(4):645-7. doi: 10.1510/icvts.2010.258368. Epub 2011 Jan 25.
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引用本文的文献

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Heart Disease and Pectus Excavatum: An Underestimated Issue-Single Center Experience and Literature Review.心脏病与漏斗胸:一个被低估的问题——单中心经验及文献综述
Life (Basel). 2024 Dec 11;14(12):1643. doi: 10.3390/life14121643.
2
Modified Ravitch procedure for pectus excavatum in Marfan syndrome with annuloaortic ectasia.针对患有主动脉根部扩张的马凡综合征患者漏斗胸的改良Ravitch手术。
Interdiscip Cardiovasc Thorac Surg. 2023 Jun 1;36(6). doi: 10.1093/icvts/ivad095.
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Simultaneous repair of congenital heart defects and pectus excavatum in young children.
幼儿先天性心脏缺陷与漏斗胸的同期修复。
Pediatr Surg Int. 2018 Mar;34(3):269-275. doi: 10.1007/s00383-017-4223-z. Epub 2018 Jan 5.