Okutur Kerem, Küçükler Kerim, Öztekın Erkan, Borlu Fatih, Erdem Levent, Demır Gökhan
Department of Internal Medicine, Section of Medical Oncology, İstanbul Bilim University, Faculty of Medicine, İstanbul.
Turk J Gastroenterol. 2010 Dec;21(4):467-9. doi: 10.4318/tjg.2010.0141.
Pheochromocytoma is a tumor of the chromaffin cells which secretes catecholamines and 90% of it originates from adrenal medulla. The main symptoms and signs are hypertension, tachycardia, sweating and headache. Rarely, acute abdomen may occur as a result of the rupture of tumoral mass or bleeding inside the mass. Here we present a 43 year old male patient who applied with acute abdominal syndrome and severe hypertension. Abdominal MRI showed a large mass hemorrhagic in nature above the right kidney. At laparotomy, ruptured adrenal mass was seen and excised successfully. The histological evaluation confirmed the diagnosis as pheochromocytoma. Ruptured adrenal pheochromocytoma is a mortal situation potentially and it should be considered in patients who present with an acute abdominal syndrome and hypertension or shock. It should be known that early diagnosis and surgery with proper preoperative treatment is a life saver.
嗜铬细胞瘤是一种起源于分泌儿茶酚胺的嗜铬细胞的肿瘤，其中90%起源于肾上腺髓质。主要症状和体征为高血压、心动过速、出汗和头痛。极少数情况下，肿瘤肿块破裂或肿块内出血可导致急腹症。在此，我们报告一名43岁男性患者，因急性腹部综合征和严重高血压前来就诊。腹部MRI显示右肾上方有一个较大的出血性肿块。剖腹手术时，发现肾上腺肿块破裂并成功切除。组织学评估确诊为嗜铬细胞瘤。肾上腺嗜铬细胞瘤破裂具有潜在致命性，对于出现急性腹部综合征和高血压或休克的患者应予以考虑。应明确的是，早期诊断并进行适当术前治疗后手术是挽救生命的关键。
