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新生儿永存性泄殖腔,表现为副柱形尿道和性别不明的生殖器。

Newborn with persistent cloaca presenting with accessory phallic urethra and ambiguous genitalia.

机构信息

Division of Pediatric Urology, McMaster Children's Hospital, McMaster University, Hamilton, Ontario, Canada.

出版信息

Urology. 2011 Sep;78(3):680-3. doi: 10.1016/j.urology.2010.12.044. Epub 2011 Feb 18.

DOI:10.1016/j.urology.2010.12.044
PMID:21334047
Abstract

Persistent cloaca is a rare urogenital anomaly that can pose significant challenges for adequate diagnosis and management. We describe the case of an infant girl with a cloacal malformation, having a single perineal orifice and an accessory phallic urethra, who presented with ambiguous genitalia at birth. The distal part of the accessory phallic urethra was used to create a mucosa-lined vestibule as a part of the total urogenital sinus mobilization. This technical maneuver allowed a more natural looking, and possibly functioning, vaginal introitus, improving the final cosmetic result.

摘要

持续性泄殖腔是一种罕见的泌尿生殖系统畸形,可能对充分诊断和管理构成重大挑战。我们描述了一例患有泄殖腔畸形的女婴病例,她有一个单一的会阴孔和一个附属的阴茎尿道,出生时表现为生殖器性别模糊。附属阴茎尿道的远端部分被用来创建一个黏膜衬里的前庭,作为总泌尿生殖窦动员的一部分。这一技术手段使阴道入口看起来更自然,也可能具有功能性,从而改善了最终的美容效果。

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Urology. 2011 Sep;78(3):680-3. doi: 10.1016/j.urology.2010.12.044. Epub 2011 Feb 18.
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