Lorente Muñoz Asís, Lisbona Alquézar María Pilar, González Martínez Luis, Sevil Navarro Jorge, Llorente Arenas Eva María
Servicio de Neurocirugía, Hospital Universitario Miguel Servet, Zaragoza, España.
Acta Otorrinolaringol Esp. 2012 May-Jun;63(3):237-40. doi: 10.1016/j.otorri.2011.01.002. Epub 2011 Feb 26.
Spontaneous herniation of brain parenchyma through a dural and osseous defect in the temporal bone is a rare entity and a bilateral form is even more infrequent. It usually presents as an intermittent but persistent otorrhea. Manifestation as nose cerebrospinal fluid (CSF) leak is very uncommon. Our objective is presenting this unusual case report of a spontaneous bilateral encephalocele with a bilateral tegmen tympani defect.