García Ron A, Jensen J, Garriga Braun C, Gómez E, Sierra J
Servicio de Pediatría, Hospital Infanta Cristina, Parla, Madrid, Spain.
An Pediatr (Barc). 2011 May;74(5):324-6. doi: 10.1016/j.anpedi.2011.01.017. Epub 2011 Mar 4.
Marin-Amat's syndrome is a rare associated movement, wherein contraction of orbicularis oculi is brought about by opening of the jaw in association with aberrant regeneration of facial nerve. This is the opposite of the Marcus-Gunn phenomenon; hence it has also been called Inverted Marcus-Gunn Phenomenon. Moreover in this case the opened the mouth or moved the jaw, the eye would close. This phenomenon is congenital and the closure of the eye is due to inhibition of the levator palpebrae superioris. We present two cases, one acquired after the surgery of tuberculosus cervical adenitis and other congenital with reference to the presentation, course and treatment. This entity is rare in children, with few reported cases, although probably will be found more frequently if looked for carefully. The diagnosis is clinical and does not require additional tests, although EMG may be useful to demonstrate the synkinesis.
马林 - 阿马特综合征是一种罕见的关联运动，即由于面神经异常再生，张口时会导致眼轮匝肌收缩。这与马库斯 - 冈恩现象相反；因此它也被称为反向马库斯 - 冈恩现象。此外，在这种情况下，张口或移动下颌时，眼睛会闭合。这种现象是先天性的，眼睛闭合是由于提上睑肌受到抑制。我们报告两例病例，一例是在颈淋巴结结核手术后获得的，另一例是先天性的，并涉及临床表现、病程和治疗。这种情况在儿童中很少见，报道的病例很少，不过如果仔细查找可能会更频繁地发现。诊断依靠临床，不需要额外检查，尽管肌电图可能有助于证明联带运动。
