Saleem Ali Faisal, Ariff Shabina, Aslam Nadeem, Ikram Mubasher
Department of Pediatrics and Child Health, The Aga Khan University Hospital, Karachi.
J Pak Med Assoc. 2010 Oct;60(10):869-72.
Congenital choanal atresia (CCA) is the developmental failure of the nasal cavity to communicate with nasopharynx. Surgical repair is recommended in the first weeks of life in bilateral cases because this is a life-threatening situation in newborns. This is a case report of a full-term, healthy newborn baby presenting with intermittent attacks of cyanosis and respiratory distress soon after birth. On examination, alternating cyanosis and normal colour was observed in the infant. The insertion of nasal catheters in both the nares revealed the diagnosis of bilateral CCA. For this rare condition, conservative management was followed with elective transnasal endoscopic repair to relieve the life threatening nasal obstruction at the tenth day of life.
先天性后鼻孔闭锁(CCA)是鼻腔与鼻咽部之间发育性的沟通障碍。双侧病例建议在出生后的头几周进行手术修复,因为这对新生儿来说是危及生命的情况。本文报告一例足月健康新生儿,出生后不久即出现间歇性青紫和呼吸窘迫发作。检查时,发现婴儿出现交替性青紫和正常肤色。双侧鼻孔插入鼻导管后确诊为双侧CCA。针对这种罕见情况,采取了保守治疗,并在出生第十天进行了择期经鼻内镜修复,以缓解危及生命的鼻阻塞。