Thoracic Oncology, Pleural Disease and Interventional Pulmonology Department, North Hospital, Marseille, France.
Eur J Cardiothorac Surg. 2011 Jun;39(6):e186-8. doi: 10.1016/j.ejcts.2011.01.074. Epub 2011 Mar 5.
Mounier-Kuhn syndrome is a rare condition that combines tracheobronchomegaly (TBM) and severe tracheobronchomalacia. Symptoms can be severe with recurrent bronchopulmonary infections and cough-induced syncope. Therapeutic management is non-specific and limited to chest physiotherapy and antibiotics during infectious exacerbations. We report a case of Mounier-Kuhn syndrome that was successfully managed by treating the posterior collapse of the central airway with yttrium aluminum pevroskyte laser. Endoscopic aspects, respiratory symptoms, and lung function tests all improved and remained stable with a follow-up of 8 years. Laser, at low power settings, could be a new therapeutic option in selected cases of tracheobronchomalacia.
Mounier-Kuhn 综合征是一种罕见的疾病，其特征为气管支气管扩张（TBM）和严重的气管支气管软化症。该病症状严重，常伴有反复发作的支气管肺部感染和咳嗽诱发的晕厥。治疗方法是非特异性的，仅限于胸部物理治疗和感染加重时使用抗生素。我们报告了一例 Mounier-Kuhn 综合征，通过钇铝石榴石激光治疗中央气道后塌，成功进行了治疗。患者的内镜表现、呼吸症状和肺功能检查均得到改善，8 年随访期间病情稳定。低功率设置的激光可能是治疗选择病例中气管支气管软化症的一种新的治疗选择。
