Best Thomas H, Vyas Himesh V, Jaquiss Robert D B, Sachdeva Ritu
Division of Pediatric Cardiology, Arkansas Children's Hospital and University of Arkansas for Medical Sciences, Little Rock, AR, USA.
Congenit Heart Dis. 2011 Jul-Aug;6(4):393-6. doi: 10.1111/j.1747-0803.2010.00477.x. Epub 2011 Mar 10.
The absence of the pulmonary valve in connection with tricuspid atresia and intact ventricular septum is a rare malformation, associated with a poor prognosis. The right ventricle is severely hypertrophied, resembling a cardiac mass protruding into the left ventricular outflow tract. We report such a case that underwent successful palliation with a Blalock-Taussig shunt followed by a superior cavopulmonary anastomosis.
与三尖瓣闭锁及室间隔完整相关的肺动脉瓣缺如是一种罕见的畸形，预后较差。右心室严重肥厚，类似一个突入左心室流出道的心脏肿物。我们报告了这样一例患者，其先行改良体肺分流术（Blalock-Taussig分流术），随后行上腔静脉-肺动脉吻合术，姑息治疗成功。
