Al-Qattan Mohammad M
Division of Plastic Surgery, King Saud University, Riyadh, Saudi Arabia.
Ann Plast Surg. 2011 Jul;67(1):90-1. doi: 10.1097/SAP.0b013e3181ee70c9.
Dorsal dimelia is a rare form of duplication along the dorsoventral axis as opposed to polydactyly and hyperphalangism, which are duplications along the radioulnar and proximodistal axes, respectively. All previous cases of dorsal dimelia involved the ulnar digits. We report the first human case of dorsal dimelia of a radial digit (index finger) in a patient with absent thumb and radial club hand. Associated anomalies of previously reported cases of dorsal dimelia are reviewed and their pathogenesis is discussed.
背侧多指畸形是一种沿背腹轴的罕见重复形式,与多指畸形和多指节畸形相反,后者分别是沿桡尺轴和近远轴的重复。既往所有背侧多指畸形病例均累及尺侧手指。我们报告了首例拇指缺如和桡侧多指(示指)畸形患者的桡侧手指背侧多指畸形病例。回顾了既往报道的背侧多指畸形病例的相关异常情况并讨论了其发病机制。