Białkowski Jacek, Rycaj Jarosław, Fiszer Roland, Głowacki Jan, Obersztyn Anna, Zyła-Frycz Maria, Szkutnik Małgorzata
Oddział Kliniczny Wrodzonych Wad Serca i Kardiologii Dziecięcej, Śląski Uniwersytet Medyczny, Śląskie Centrum Chorób Serca, Zabrze.
Kardiol Pol. 2011;69(3):302-4.
We present a case of a 21 year-old man who has had Fontan type correction 17 years ago with symptoms of severe heart insufficiency (III NYHA class, cahectic, with massive peripheral oedema and ascites) caused by increased pulmonary vascular resistance and increased pulmonary artery pressure. He was treated successfully with long term sildenafil medication.
我们报告一例21岁男性患者,其17年前接受了Fontan类矫正手术,现因肺血管阻力增加和肺动脉压力升高出现严重心力衰竭症状(纽约心脏协会III级,恶病质,伴有大量外周水肿和腹水)。他通过长期服用西地那非成功治愈。