Amirghofran Ahmad Ali, Karimi Ashkan, Ajami Gholam Hossein, Rasekhi Alireza
University of Florida, Division of Thoracic and Cardiovascular Surgery, Gainesville, FL, USA.
J Cardiothorac Surg. 2011 Mar 30;6:41. doi: 10.1186/1749-8090-6-41.
An 8-year-old girl was admitted for a simple closure of echocardiographically diagnosed Atrial Septal Defect (ASD). During the operation the right pulmonary veins orifices were not detected in the left atrium and attempt to localize them led to the discovery of three additional anomalies, namely Interrupted Inferior Vena Cava (IIVC), Scimitar syndrome, and systemic arterial supply of the lung. Postoperatively these finding were confirmed by CT angiography. This case report emphasizes the need for adequate preoperative diagnosis and presents a very rare constellation of four congenital anomalies that to the best of our knowledge is not reported before.
一名8岁女孩因超声心动图诊断的房间隔缺损（ASD）行单纯修补术入院。手术过程中，在左心房未发现右肺静脉开口，试图定位时发现了另外三种异常，即下腔静脉中断（IIVC）、弯刀综合征和肺的体循环动脉供血。术后CT血管造影证实了这些发现。本病例报告强调了充分术前诊断的必要性，并呈现了一组非常罕见的四种先天性异常组合，据我们所知，此前尚未有相关报道。
