Agarwal Kiran, Goel Ruchika Kumar, Puri Vandana
Department of Pathology, Lady Hardinge Medical College, New Delhi, India.
Turk Patoloji Derg. 2011 Jan;27(1):84-6.
Rhabdomyosarcoma is a soft tissue neoplasm arising from primitive embryonal mesenchyma. Embryonal rhabdomyosarcoma mostly affects children younger than 10 years of age, but it also occurs in adolescents and young adults. Pleomorphic rhabdomyosarcoma is a rare variant that almost always arises in adults older than 45 years of age. Mesentery is a rare site for botyroid embryonal rhabdomyosarcoma and on extensive search we found only one case of a botryoid rhabdomyosarcoma in a child of 2 years. We report a rare case of botyroid embryonal rhabdomyosarcoma occurring in the mesentery of a 30 year old female.
横纹肌肉瘤是一种起源于原始胚胎间充质的软组织肿瘤。胚胎性横纹肌肉瘤主要影响10岁以下儿童,但也见于青少年和年轻成年人。多形性横纹肌肉瘤是一种罕见的变异型,几乎总是发生于45岁以上的成年人。肠系膜是葡萄状胚胎性横纹肌肉瘤的罕见发病部位,经广泛检索,我们仅发现1例2岁儿童的葡萄状横纹肌肉瘤病例。我们报告1例罕见的发生于30岁女性肠系膜的葡萄状胚胎性横纹肌肉瘤病例。