Lim Hui-Ying, Bodmer Rolf
Development and Aging Program, Neuroscience, Aging and Stem Cell Research Center, Sanford-Burnham Medical Research Institute, La Jolla, CA, USA.
Fly (Austin). 2011 Jul-Sep;5(3):234-6. doi: 10.4161/fly.5.3.15708. Epub 2011 Jul 1.
Obesity has reached pandemic proportions globally and is often associated with lipotoxic heart diseases. In the obese state, caloric surplus is accommodated in the adipocytes as triglycerides. As the storage capacity of adipocytes is exceeded or malfunctioning, lipids begin to infiltrate and accumulate in non-adipose tissues, including the myocardium of the heart, leading to organ dysfunction. While the disruption of caloric homeostasis has been widely viewed as a principal mechanism in contributing to peripheral tissue steatosis and lipotoxicity, our recent studies in Drosophila have led to the novel finding that deregulation of phospholipid homeostasis may also significantly contribute to the pathogenesis of lipotoxic cardiomyopathy. Fly mutants that bear perturbations in phosphatidylethanolamine (PE) biosynthesis, such as the easily-shocked (eas) mutants defective in ethanolamine kinase, incurred aberrant activation of the sterol regulatory element binding protein (SREBP) pathway, thereby causing chronic lipogenesis and cardiac steatosis that culminates in the development of lipotoxic cardiomyopathy. Here, we describe the potential relationship between SREBP and other eas-associated phenotypes, such as neuronal excitability defects. We will further discuss the additional implications presented by our work toward the effects of altered lipid metabolism on cellular growth and/or proliferation in response to defective phospholipid homeostasis.
肥胖在全球已达到流行程度,且常与脂毒性心脏病相关。在肥胖状态下,热量过剩以甘油三酯的形式存储在脂肪细胞中。当脂肪细胞的存储能力被超过或出现功能故障时,脂质开始渗入并在包括心脏心肌在内的非脂肪组织中积累,导致器官功能障碍。虽然热量稳态的破坏已被广泛视为导致外周组织脂肪变性和脂毒性的主要机制,但我们最近在果蝇中的研究有了新发现,即磷脂稳态失调也可能显著促成脂毒性心肌病的发病机制。在磷脂酰乙醇胺(PE)生物合成中存在扰动的果蝇突变体,如在乙醇胺激酶方面有缺陷的易受惊吓(eas)突变体,会引发固醇调节元件结合蛋白(SREBP)途径的异常激活,从而导致慢性脂肪生成和心脏脂肪变性,最终发展为脂毒性心肌病。在此,我们描述了SREBP与其他 eas 相关表型(如神经元兴奋性缺陷)之间的潜在关系。我们还将进一步讨论我们的工作对脂质代谢改变在响应磷脂稳态缺陷时对细胞生长和/或增殖的影响所带来的其他启示。